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Paediatric keratoconus : an ERN-EYE clinical consensus statement on diagnosis, treatment and follow-up care
ID Buzzonetti, Luca (Avtor), ID Mazzotta, Cosimo (Avtor), ID Iester, Michele (Avtor), ID Pauklin, Mikk (Avtor), ID Boehringer, Daniel (Avtor), ID Zemaitiene, Reda (Avtor), ID Vannucchi, Martino (Avtor), ID Cocho, Lidia (Avtor), ID Studeny, Pavel (Avtor), ID Gavard, Amélie (Avtor), ID Tekavčič Pompe, Manca (Avtor)

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Izvleček
This clinical consensus statement, developed through the European Reference Network for Rare Eye Diseases (ERN-EYE), provides recommendations for the diagnosis, monitoring and management of paediatric keratoconus. Paediatric keratoconus is a corneal ectasia that typically presents during childhood or adolescence, often advancing rapidly and significantly affecting visual development. Despite its impact, standardised paediatric-specific guidelines are lacking. A multidisciplinary panel of experts from across Europe contributed to this statement through a structured Delphi process. The consensus reviews the current understanding of the physiopathology, diagnostic criteria, risk factors and classification systems of paediatric keratoconus. It outlines strategies for early detection and monitoring, emphasises the role of patient and family education and presents current treatment approaches, with specific recommendations for paediatric care. The aim of this document is to guide ophthalmologists, paediatricians and associated professionals in delivering timely and appropriate care, improving outcomes for children with keratoconus across Europe.

Jezik:Angleški jezik
Ključne besede:cross-linking, keratoconus, keratoplasty, paediatric keratoconus, rare diseases, guidelines
Vrsta gradiva:Članek v reviji
Tipologija:1.02 - Pregledni znanstveni članek
Organizacija:MF - Medicinska fakulteta
Status publikacije:Objavljeno
Različica publikacije:Objavljena publikacija
Leto izida:2026
Št. strani:Str. 2825-2861
Številčenje:Vol. 15, iss. 9
PID:20.500.12556/RUL-186918 Povezava se odpre v novem oknu
UDK:617.7
ISSN pri članku:2193-6528
DOI:10.1007/s40123-026-01463-5 Povezava se odpre v novem oknu
COBISS.SI-ID:287886083 Povezava se odpre v novem oknu
Datum objave v RUL:07.09.2026
Število ogledov:80
Število prenosov:32
Metapodatki:XML DC-XML DC-RDF
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Gradivo je del revije

Naslov:Ophthalmology and therapy
Založnik:Springer Nature
ISSN:2193-6528
COBISS.SI-ID:526708249 Povezava se odpre v novem oknu

Licence

Licenca:CC BY-NC 4.0, Creative Commons Priznanje avtorstva-Nekomercialno 4.0 Mednarodna
Povezava:http://creativecommons.org/licenses/by-nc/4.0/deed.sl
Opis:Licenca Creative Commons, ki prepoveduje komercialno uporabo, vendar uporabniki ne rabijo upravljati materialnih avtorskih pravic na izpeljanih delih z enako licenco.

Sekundarni jezik

Jezik:Slovenski jezik
Ključne besede:križno povezovanje, keratokonus, keratoplastika, pediatrični keratokonus, redke bolezni, smernice

Projekti

Financer:EC - European Commission
Številka projekta:101085439
Naslov:ERN-EYE 22–23
Akronim:ERN-EYE

Financer:HADEA
Številka projekta:84498

Financer:EC - European Commission
Številka projekta:101155859
Naslov:ERN-EYE 2023-2027
Akronim:ERN-EYE

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