20.500.12556/RUL-99056 Primarna imunska pomanjkljivost pri otroku pregled literature Primary immunodeficiency diseases in child literature review Uvod:Primarna imunska pomanjkljivost je skupina genetskih motenj, ki se kažejo kot nepravilno delovanje elementov imunskega sistema. V prvi vrsti se kaže s ponavljajočimi okužbami. Otroci se zdravijo z nadomestno terapijo imunoglobulinov, ki jo prejemajo intravenozno ali subkutano. Pri zdravljenju otroka imajo pomembno vlogo tudi starši, ki jih mora medicinska sestra vključiti v zdravljenje. Namen: Namen diplomskega dela je predstaviti primarno imunsko pomanjkljivost pri otroku. Cilji diplomskega dela so opisati: bolezni primarne imunske pomanjkljivosti, zdravljenje z imunoglobulini, vlogo medicinske sestre in kakovost življenja s primarno imunsko pomanjkljivostjo. Metode: V diplomskem delu je bila uporabljena deskriptivna metoda dela s pregledom strokovne in znanstvene literature v slovenskem in angleškem jeziku, med letom 2010 in 2016. Uporabljene so bile podatkovne baze CINAHL, Google Scholar, MedlinePlus. Razprava in sklep: Bolezni primarne imunske pomanjkljivosti so vsak dan bolj prepoznavna skupina bolezni. Načini zdravljenja se izboljšujejo in otrokom omogočajo bolj kakovostno in samostojno življenje. Medicinska sestra ima poleg priprave in aplikacije terapije, pomembno vlogo pri zdravstveni vzgoji, nudenju opore, pomoči otrokom in staršem, ki se zaradi bolezni soočajo z novo nastalimi odgovornostmi. Introduction: Primary immunodeficiency is a group of genetic disorders manifested as an improper activity of immune system elements. Its most common clinical signs are recurrent infections. Children are treated with immunoglobulin replacement therapy, which they can receive intravenously or subcutaneously. Parents also play an important role in the child’s care therefore a nurse must include them into the treatment plan. Aim of this thesis: To introduce primary immunodeficiency diseases in child. The objective of this study is to describe primary immunodeficiency, treatment with immunoglobulin, a nurse’s role in the treatment and the quality of life with such a disease. Methods: A descriptive method of work was used based on a review of foreign and domestic scientific and professional literature published between 2010 and 2016. Remote access databases CINAHL, Google Scholar, MedlinePlus were used. Discussion and conclusion: Primary immunodeficiency diseases have become a growingly recognizable group of diseases through years. Treatment options are improving and they enable a better quality of children's lives and their greater autonomy. A nurse has to prepare treatment and make sure it is appropriately applied. She also has an important role in the health education, giving support, helping the parents and children who have to face a new kind of responsibility due to their disease. primarna imunska pomanjkljivost vloga medicinske sestre imunoglobulini kakovost življenj primary immunodeficiency nurse’s role immunoglobulin quality of life true false false Slovenski jezik Angleški jezik Diplomsko delo/naloga 2017-12-23 07:15:19 2017-12-23 07:15:22 2022-08-16 10:31:24 0000-00-00 00:00:00 2017 0 0 0000-00-00 NiDoloceno NiDoloceno NiDoloceno 0000-00-00 0000-00-00 0000-00-00 81751 5381739 3018.pdf 3018.pdf 1 6E0C76697FA5070E3F7602132C886753 7b8053e3848af9c825a43ae8e66f9d0b7b66635d239172089481239cd059c63b 7c94c4bf-a1b4-11eb-a523-00155dcfd717 20.500.12556/rul/88df9849-ba8c-4364-bdda-81a8be37c879 https://repozitorij.uni-lj.si/Dokument.php?lang=slv&id=108405 Zdravstvena fakulteta 0 0 0